Total colonic aganglionosis (with or without ileal involvement): a review of 27 cases.

@article{NFkt1986TotalCA,
  title={Total colonic aganglionosis (with or without ileal involvement): a review of 27 cases.},
  author={C N-F{\'e}k{\'e}t{\'e} and Claude C Ricour and H{\'e}l{\'e}ne Martelli and Sony Jacob and Denys Pellerin},
  journal={Journal of pediatric surgery},
  year={1986},
  volume={21 3},
  pages={251-4}
}
From 1960 to 1984, 27 cases of total colonic aganglionosis were treated at the Sick Children's Hospital in Paris; in 19 cases there was ileal involvement, 16 of them extending more than 15 cm above the ileocecal valve. Five had a family history of Hirschsprung's disease. Nine infants died without having had definitive surgery, because of delayed diagnosis, or intractable malabsorption in extensive ileal aganglionosis. Two cases were diagnosed only at the ages of 6 and 13 years. Eleven children… CONTINUE READING