Therapeutic approach for patients with catecholaminergic polymorphic ventricular tachycardia: state of the art and future developments.

@article{Werf2012TherapeuticAF,
  title={Therapeutic approach for patients with catecholaminergic polymorphic ventricular tachycardia: state of the art and future developments.},
  author={Christian van der Werf and Aeilko H. Zwinderman and Arthur A. M. Wilde},
  journal={Europace : European pacing, arrhythmias, and cardiac electrophysiology : journal of the working groups on cardiac pacing, arrhythmias, and cardiac cellular electrophysiology of the European Society of Cardiology},
  year={2012},
  volume={14 2},
  pages={175-83}
}
Catecholaminergic polymorphic ventricular tachycardia (CPVT) is an inherited arrhythmia syndrome characterized by bidirectional or polymorphic ventricular arrhythmias under conditions of increased sympathetic activity in young patients with structurally normal hearts. Patients with CPVT are at high risk of developing life-threatening ventricular arrhythmias when untreated. A wide variety of arrhythmic event rates on conventional therapy, with β-blockers as the cornerstone, has been reported… CONTINUE READING