The origin of tubular aggregates in human myopathies

@article{Chevessier2005TheOO,
  title={The origin of tubular aggregates in human myopathies},
  author={F. Chevessier and St{\'e}phanie Bauch{\'e}-Godard and J. Leroy and J. Koenig and M. Paturneau-Jouas and B. Eymard and D. Hantaı̈ and M. Verdi{\'e}re-Sahuqu{\'e}},
  journal={The Journal of Pathology},
  year={2005},
  volume={207}
}
Tubular aggregates are morphological abnormalities characterized by the accumulation of densely packed tubules in skeletal muscle fibres. To improve knowledge of tubular aggregates, the formation and role of which are still unclear, the present study reports the electron microscopic analysis and protein characterization of tubular aggregates in six patients with ‘tubular aggregate myopathy’. Three of the six patients also presented with myasthenic features. A large panel of immunochemical… Expand
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