The oral health needs of children, adolescents and young adults affected by a mucopolysaccharide disorder.

@article{James2012TheOH,
  title={The oral health needs of children, adolescents and young adults affected by a mucopolysaccharide disorder.},
  author={Alison R James and Christian J. Hendriksz and O. L. Addison},
  journal={JIMD reports},
  year={2012},
  volume={2},
  pages={51-8}
}
BACKGROUND As one of the 4 United Kingdom national centres for Lysosomal Storage Disorders, Birmingham Children's Hospital (BCH) cares for 49 patients with a mucopolysaccharide (MPS) disorder. Presently, their oral health needs have never been fully investigated. Enzyme therapies are revolutionising medical treatment, and will prolong life expectancy. Therefore, oral health and its impact on quality of life are increasingly important. HYPOTHESIS Patients with an MPS disorder have greater oral… CONTINUE READING

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