The differential diagnosis of chorea
@article{Wild2007TheDD, title={The differential diagnosis of chorea}, author={Edward J. Wild and Sarah J. Tabrizi}, journal={Practical Neurology}, year={2007}, volume={7}, pages={360 - 373} }
Chorea is a hyperkinetic movement disorder characterised by excessive spontaneous movements that are irregularly timed, randomly distributed and abrupt. In this article, the authors discuss the causes of chorea, particularly Huntington’s disease and the genetic syndromes that may resemble it, including HDL1-3, inherited prion disease, spinocerebellar ataxias 1, 3 and 17, neuroacanthocytosis, dentatorubro-pallidoluysian atrophy (DRPLA), brain iron accumulation disorders, Wilson’s disease, benign…
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