The Varieties of Auditory Neuropathy

@article{Starr2000TheVO,
  title={The Varieties of Auditory Neuropathy},
  author={Arnold Starr and Yvonne S. Sininger and Hillel Pratt},
  journal={Journal of Basic and Clinical Physiology and Pharmacology},
  year={2000},
  volume={11},
  pages={215 - 230}
}
Auditory neuropathy (AN) was initially described as impairment of auditory neural function, with preserved cochlear hair cell function. In this report, 67 patients with audiological and neurophysiological criteria for hearing loss due to auditory neuropathy are described. Reviewing this large body of patients, AN appears to consist of a number of varieties, with different etiologies and sites affected. All varieties share a relatively spared receptor function, and an impaired neural response… 
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It can be concluded that differences in cochlear implant outcome or hearing aid use in patients with AN are related to the pathophysiological mechanisms underlying alteration of auditory nerve discharge associated with individual etiologies.
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