The ALSFRS-R: a revised ALS functional rating scale that incorporates assessments of respiratory function

@article{Cedarbaum1999TheAA,
  title={The ALSFRS-R: a revised ALS functional rating scale that incorporates assessments of respiratory function},
  author={Jesse M. Cedarbaum and Nancy Stambler and Errol Malta and Cynthia Fuller and Dana C. Hilt and Barbara Thurmond and Arline Nakanishi},
  journal={Journal of the Neurological Sciences},
  year={1999},
  volume={169},
  pages={13-21}
}
The ALS Functional Rating Scale (ALSFRS) is a validated rating instrument for monitoring the progression of disability in patients with amyotrophic lateral sclerosis (ALS). One weakness of the ALSFRS as originally designed was that it granted disproportionate weighting to limb and bulbar, as compared to respiratory, dysfunction. We have now validated a revised version of the ALSFRS, which incorporates additional assessments of dyspnea, orthopnea, and the need for ventilatory support. The… Expand

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