The 17p-syndrome: a distinct myelodysplastic syndrome entity?

@article{Jary1997The1A,
  title={The 17p-syndrome: a distinct myelodysplastic syndrome entity?},
  author={L. Jary and H. Mossafa and C. Fourcade and P. Genet and M. Pulik and G. Flandrin},
  journal={Leukemia & lymphoma},
  year={1997},
  volume={25 1-2},
  pages={
          163-8
        }
}
  • L. Jary, H. Mossafa, +3 authors G. Flandrin
  • Published 1997
  • Medicine
  • Leukemia & lymphoma
    • The 17p- syndrome is a subset of myelodysplastic syndrome characterized by "typical" dysgranulopoïesis, combining a pseudo-Pelger-Hüet and a deletion of the short arm of chromosome 17. We describe two patients; one with de novo myelodysplastic syndrome (RAEB), one with secondary MDS (RAEB-T). Both showed a 17p- deletion resulting from tanslocations involving 17p associated with an additional complex cytogenetics, and both of them had a particular type of dysgranulopoiesis, combining pseudo… CONTINUE READING
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    Background Citations
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    Methods Citations
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