THE CLINICAL PRESENTATION OF EHLERS‐DANLOS SYNDROME

@article{Lawrence2005THECP,
  title={THE CLINICAL PRESENTATION OF EHLERS‐DANLOS SYNDROME},
  author={Elizabeth J Lawrence},
  journal={Advances in Neonatal Care},
  year={2005},
  volume={5},
  pages={301–314}
}
  • E. J. Lawrence
  • Published 1 December 2005
  • Medicine
  • Advances in Neonatal Care

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...

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Symptoms and genetic basis of Ehlers-Danlos syndrome, suggestions for management, and resources available for health care providers, families, and patients with EDS are provided.

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Although most affected patients survive the first and second major complications, Ehlers-Danlos syndrome type IV results in premature death, and the diagnosis should be considered in young people who come to medical attention because of uterine rupture during pregnancy or arterial or visceral rupture.

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