Syndrome of intrahepatic biliary dysgenesis and cardiovascular malformations.

@article{Greenwood1976SyndromeOI,
  title={Syndrome of intrahepatic biliary dysgenesis and cardiovascular malformations.},
  author={Ronald D Greenwood and Amnon Rosenthal and Allen C. Crocker and Alexander S. Nadas},
  journal={Pediatrics},
  year={1976},
  volume={58 2},
  pages={243-7}
}
Peripheral pulmonary stenosis with or without intracardiac disease is described in 14 patients with intrahepatic biliary dysgenesis. Cardiovascular malformations were not present among a large group of patients with extrahepatic biliary dysgenesis. This association of intrahepatic biliary dysgenesis and vascular malformations is postulated to be a specific malformation syndrome resulting most probably from intrauterine infection. The cardiovascular disease is usually mild. The liver dysfunction… CONTINUE READING

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