Sustained high plasma mannose less sensitive to fluctuating blood glucose in glycogen storage disease type Ia children

@article{Nagasaka2012SustainedHP,
  title={Sustained high plasma mannose less sensitive to fluctuating blood glucose in glycogen storage disease type Ia children},
  author={H. Nagasaka and T. Yorifuji and R. Bandsma and Tomozumi Takatani and Hisaki Asano and H. Mochizuki and M. Takuwa and H. Tsukahara and A. Inui and Tomoyuki Tsunoda and H. Komatsu and Eitaro Hiejima and T. Fujisawa and K. Hirano and T. Miida and A. Ohtake and T. Taguchi and I. Miwa},
  journal={Journal of Inherited Metabolic Disease},
  year={2012},
  volume={36},
  pages={75-81}
}
  • H. Nagasaka, T. Yorifuji, +15 authors I. Miwa
  • Published 2012
  • Biology, Medicine
  • Journal of Inherited Metabolic Disease
  • Plasma mannose is suggested to be largely generated from liver glycogen-oriented glucose-6-phosphate. This study examined plasma mannose in glycogen storage disease type Ia (GSD Ia) lacking conversion of glucose-6-phosphate to glucose in the liver. We initially examined fasting—and postprandial 2 h—plasma mannose and other blood carbohydrates and lipids for seven GSD Ia children receiving dietary interventions using cornstarch and six healthy age-matched children. Next, one-day successive intra… CONTINUE READING

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