Successful Heart Transplantation for Unreversible Endomyocardial Fibrosis Related to FIP1L1-PDGFRA Chronic Eosinophilic Leukemia.

@article{Fassnacht2015SuccessfulHT,
  title={Successful Heart Transplantation for Unreversible Endomyocardial Fibrosis Related to FIP1L1-PDGFRA Chronic Eosinophilic Leukemia.},
  author={F. Fassnacht and Mathilde Roumier and Pierre Jean Fouret and Vincent Lévy and Shaida Varnous and St{\'e}phanie Russel and Guillaume Lef{\`e}vre and Jean-Emmanuel Kahn},
  journal={Transplantation},
  year={2015},
  volume={99 11},
  pages={
          e176-7
        }
}
Endomyocardial fibrosis (EMF) is estimated to be the most frequent worldwide cause of restrictive cardiomyopathy with impaired filling of 1 or both ventricles caused by deposition of fibrous tissue on endocardial surfaces. The etiology is still unknown, but allergy, malnutrition, helminthic infestations, cardiotropic virus, and toxic agents have been related to EMF. The main causes of nontropical EMF are eosinophilic granulomatosis with polyangiitis (or ChurgStrauss) and hypereosinophilic… Expand
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