Substrate utilization during and after exercise in mild cystic fibrosis.

@article{Wideman2009SubstrateUD,
  title={Substrate utilization during and after exercise in mild cystic fibrosis.},
  author={Laurie Wideman and Carol F. Baker and Pam Kocher Brown and Leslie A Consitt and Walter T. Ambrosius and Michael S. Schechter},
  journal={Medicine and science in sports and exercise},
  year={2009},
  volume={41 2},
  pages={
          270-8
        }
}
PURPOSE To determine substrate utilization and energy expenditure during maximal and submaximal exercise and recovery in adolescents with cystic fibrosis (CF) and healthy age-matched controls (C). METHODS Ten clinically stable CF patients (four girls, six boys; age = 10-22 yr) were matched by body mass index, age, gender, and Tanner stage to healthy controls. Subjects completed VO(2peak) testing and submaximal exercise (20 min) on a cycle ergometer at a relative intensity of 50% VO2(peak) and… 
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Supra-maximal verification of peak oxygen uptake in adolescents with cystic fibrosis
Supramaximal Verification of Peak Oxygen Uptake in Adolescents With Cystic Fibrosis
TLDR
The O2 peak measured in CPET seems to reflect the true O2-peak in adolescents with CF, as it resulted in comparable cardiorespiratory peak values between the maximal and non-maximal effort groups.
Validity of the oxygen uptake efficiency slope in children with cystic fibrosis and mild-to-moderate airflow obstruction.
TLDR
The OUES is not a valid submaximal measure of cardiopulmonary exercise capacity in children with mild to moderate CF, due to its limited distinguishing properties, its nonlinearity throughout progressive exercise, and its moderate correlation with VO(2peak) and the ventilatory threshold.
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TLDR
The data show that children with mild-to-moderate CF have the capability to perform HIE and 24 h allows sufficient time for recovery, and following HIE the metabolic and perceptual responses to MIE in both groups decreased 24 h later during test 3.
Ventilatory response to exercise in adolescents with cystic fibrosis and mild-to-moderate airway obstruction
TLDR
An exaggerated ventilatory response (high VE/WR ratio values), which was adequate for CO2 exhalation during progressive exercise up to maximal exhaustion in CF patients with mild-to-moderate airway obstruction is found.
Assessment and interpretation of aerobic exercise (dys)function in paediatric patients with cystic fibrosis
TLDR
There is a need for further well-powered research directly comparing the accuracy of the Godfrey protocol, SRT, ramp testing and a combined ramp and Smax protocol to determine V̇O2max, in addition to the other key parameters of aerobic exercise function, in paediatric and adult patients with CF.
Diet, Food, Nutrition, and Exercise in Cystic Fibrosis
Overall and differentiated sensory responses to cardiopulmonary exercise test in patients with cystic fibrosis: kinetics and ability to predict peak oxygen uptake
TLDR
Submaximal RPE scores obtained during CPET can provide acceptable estimate of V˙O2peak in adults with CF, particularly in those having significant exercise intolerance, and future studies should assess whether the prediction can be improved.
The PWC170: comparison of different stage lengths in 11–16 year olds
TLDR
PWC170 showed moderate associations with VO2peak, with the 2-min protocol showing the best correlation, and the three PWC170 protocols differ significantly; therefore, it is not advisable to directly compare results from different protocols.
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References

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