Status marmoratus and Bielschowsky bodies. A report of two cases and review of the literature.

@article{Adler1982StatusMA,
  title={Status marmoratus and Bielschowsky bodies. A report of two cases and review of the literature.},
  author={Deborah Adler and Dikran S. Horoupian and Javad Towfighi and Angelo Gandolfi and Kinuko Suzuki},
  journal={Acta neuropathologica},
  year={1982},
  volume={56 1},
  pages={75-7}
}
Intraneuronal inclusions, consisting of polyglucosan and having histochemical and ultrastructural features identical to Lafora body of familial myoclonic epilepsy (Unverricht-Lafora disease), have been found restricted to the lateral pallidum in five patients. Two of these patients were also found to have status marmoratus of the basal ganglia. These lateral pallidal inclusions have been named after Bielschowsky, their original discoverer. We report two additional patients with status… CONTINUE READING