A 54-year-old Canadian presented with a 1-month history of painless swelling in the right testis. The diagnosis was thought to be a sperm granuloma, a leiomyoma, or an adenomatoid tumour of the epididymis; histologic examination, however, revealed evidence of schistosomiasis, probably due to Schistosoma haematobium. Solitary schistosomiasis of the epididymis has been reported previously in only two cases. Epididymal schistosomiasis has never been diagnosed preoperatively because it is so rare, but even if it were suspected preoperatively and confirmed by biopsy, chemotherapy alone would not prevent impairment of epididymal function due to scarring. Surgical excision of the lesion, therefore, is recommended.