Sjögren-Larsson syndrome: postmortem brain abnormalities.


Brain abnormalities were described in a patient who had experienced Sjogren-Larsson syndrome (SLS) with typical clinical signs. Examination of the brain revealed (1) accumulation of peculiar lipoid substances stained lightly with periodic acid-Schiff (PAS) in the subpial, subependymal, and perivascular glial layers, the subpial and perivascular spaces, and… (More)


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@article{Yamaguchi1998SjgrenLarssonSP, title={Sj{\"o}gren-Larsson syndrome: postmortem brain abnormalities.}, author={K. Yamaguchi and Tango Handa}, journal={Pediatric neurology}, year={1998}, volume={18 4}, pages={338-41} }