Sildenafil therapy in complex pulmonary atresia with pulmonary arterial hypertension.

@article{Lim2008SildenafilTI,
  title={Sildenafil therapy in complex pulmonary atresia with pulmonary arterial hypertension.},
  author={Zek S Lim and Joseph J Vettukattill and Anthony P. Salmon and Gruschen R. Veldtman},
  journal={International journal of cardiology},
  year={2008},
  volume={129 3},
  pages={339-43}
}
BACKGROUND Complex pulmonary atresia (CPA) i.e. pulmonary atresia with ventricular septal defect and major aorto-pulmonary collaterals (MAPCAs) or Tetralogy of Fallot with MAPCAs frequently have a clinical course complicated by development of pulmonary arterial (PA) hypertension. METHODS A cross-sectional retrospective review of patients >16 years with CPA or Tetralogy of Fallot with MAPCAs and PA hypertension treated with sildenafil was conducted. Case notes were reviewed for baseline and… CONTINUE READING