Short QT syndrome: a very rare arrhythmogenic entity.

  title={Short QT syndrome: a very rare arrhythmogenic entity.},
  author={Osman Can Yontar and Kenan Yalta and Mehmet Yilmaz and Okan Onur Turgut},
  journal={Acta cardiologica},
  volume={63 5},
Short QT syndrome (SQTS) is a gene-related arrhythmogenic syndrome harbouring a large spectrum of symptoms ranging from mild palpitations to sudden cardiac death.The mutation of genes (KCNH2, KCNQ1, and KCNJ2) encoding for cardiac potassium channels plays a central role in SQTS. Electrocardiography is the primary important step in the diagnosis (short QT interval along with T wave changes), but ECG findings may be easily ignored. Treatment of the syndrome is still controversial. Some specific… CONTINUE READING