Severe combined immunodeficiency: A cohort of 40 patients

@article{Yeganeh2008SevereCI,
  title={Severe combined immunodeficiency: A cohort of 40 patients},
  author={M Zabihi Yeganeh and Marzieh Heidarzade and Zahra Pourpak and Nima Parvaneh and Nima Rezaei and Mohammad Javad Gharagozlou and Masoud Movahedi and Mahnaz Sadeghi Shabestari and Setareh Mamishi and Asghar Aghamohammadi and Mostafa Moin},
  journal={Pediatric Allergy and Immunology},
  year={2008},
  volume={19}
}
Severe Combined Immunodeficiency (SCID) consists of a heterogeneous group of genetic disorders characterized by an arrest in T lymphocyte development which is variably associated with an abnormal differentiation of B and NK cells. In order to depict the clinical state of Iranian patients with SCID, records of forty patients were reviewed. Patients were classified based on the flow cytometry data in two groups of B− and B+. In thirty two families (80%) parents were consanguine and in 17 families… 
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