Segmental absence of intestinal muscle with ileal web in an extremely low birth weight infant: case report.

@article{Buyuktiryaki2016SegmentalAO,
  title={Segmental absence of intestinal muscle with ileal web in an extremely low birth weight infant: case report.},
  author={Mehmet Buyuktiryaki and Hayriye Gozde Kanmaz and Nil{\"u}fer Okur and Ufuk Ateş and Ali Levent Şirvan and Nurdan Uraş},
  journal={Archivos argentinos de pediatria},
  year={2016},
  volume={114 2},
  pages={
          e108-10
        }
}
Spontaneous intestinal perforations are localized perforations without the typical clinical, radiological, and histopathological features of necrotizing enterocolitis. Spontaneous intestinal perforation is a recently defined clinical entity. The best-known risk factor is prematurity. It is seen 2-3% in very low birthweight infants and 5 % of extremely low birthweight infants. Herein we report an extremely low birthweight infant with spontaneous intestinal perforation, segmental absence of… 
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References

SHOWING 1-10 OF 10 REFERENCES

The mechanism of focal intestinal perforations in neonates with low birth weight

TLDR
The histology of the latest consecutive infants diagnosed as having meconium peritonitis (MP) due to in-utero volvulus and perforation is examined and it is speculated that thinning or absence of the intestinal musculature in FIP may be a result of a transient ischemic event occurring in-UTero and that FIP might develop in the damaged intestine after birth when it is fully dilated.

Spontaneous, isolated intestinal perforations in neonates with birth weight less than 1,000 g not associated with necrotizing enterocolitis.

TLDR
It is concluded that intestinal perforation can occur in the absence of NEC; bluish discoloration of the abdomen is the most reliable clinical finding; and perforations may be associated with coagulase-negative staphylococcal infection.

Segmental absence of intestinal musculature with intestinal atresia and ileal perforation.

TLDR
Sir,Intestinal obstruction is a common cause for emergency surgical intervention in the newborn infant and accounts for about one-third of all cases of neonatal intestinal obstructi...

Surgical Management of Extremely Low Birth Weight Infants with Neonatal Bowel Perforation: A Single-Center Experience and a Review of the Literature

TLDR
The treatment approach was associated with low mortality and developmental delay seems to be caused by extreme prematurity rather than NEC- or FIP-related bowel perforation.

Postoperative Outcomes of Extremely Low Birth-Weight Infants With Necrotizing Enterocolitis or Isolated Intestinal Perforation: A Prospective Cohort Study by the NICHD Neonatal Research Network

TLDR
A distinction can be made preoperatively between NEC and IP based on abdominal radiographic findings and the patient's age at operation, and future randomized trials that compare laparotomy versus drainage would likely benefit from stratification of treatment assignment based on preoperative diagnosis.

Laparotomy versus peritoneal drainage for necrotizing enterocolitis and perforation.

TLDR
The type of operation performed for perforated necrotizing enterocolitis does not influence survival or other clinically important early outcomes in preterm infants.

Epidemiology of small intestinal atresia in Europe: a register-based study

TLDR
There was weak evidence of an increased risk of SIA in mothers aged less than 20 years compared with mothers aged 20 to 29 years, although SIA and duodenal atresia prevalence varied significantly between registers.