Schnitzler Syndrome With Response to Anakinra Monotherapy: 7 Years of Follow-up.

Schnitzler syndrome is a rare entity, with around 250 cases reported to date. It is characterized by the presence of an urticarial rash associated with a monoclonal gammopathy, together with recurrent episodes of fever, joint pain, generalized bone pain, lymphadenopathy, hepatosplenomegaly, and bone changes. Although its etiology and pathogenesis remain… CONTINUE READING