Scale for the assessment and rating of ataxia

@article{SchmitzHbsch2006ScaleFT,
  title={Scale for the assessment and rating of ataxia},
  author={Tanja Schmitz-H{\"u}bsch and Sophie T{\'e}zenas du Montcel and L{\'a}szl{\'o} Balik{\'o} and Jos{\'e} Berciano and Sylvia Boesch and Chantal Depondt and Paola Giunti and Christoph Globas and Jon Infante and J. S. Kang and B Kremer and Caterina Mariotti and B{\'e}la Melegh and Massimo Pandolfo and Maryla Rakowicz and Pascale Ribai and Rafał Rola and L. Sch{\"o}ls and Sandra Szymanski and Bart P.C. Van de Warrenburg and Alexandra D{\"u}rr and Thomas Klockgether},
  journal={Neurology},
  year={2006},
  volume={66},
  pages={1717 - 1720}
}
Objective: To develop a reliable and valid clinical scale measuring the severity of ataxia. Methods: The authors devised the Scale for the Assessment and Rating of Ataxia (SARA) and tested it in two trials of 167 and 119 patients with spinocerebellar ataxia. Results: The mean time to administer SARA in patients was 14.2 ± 7.5 minutes (range 5 to 40). Interrater reliability was high, with an intraclass coefficient (ICC) of 0.98. Test-retest reliability was high with an ICC of 0.90. Internal… 

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References

SHOWING 1-10 OF 12 REFERENCES
Reliability and validity of the International Cooperative Ataxia Rating Scale: A study in 156 spinocerebellar ataxia patients
TLDR
Although validity testing was limited, there was evidence of validity of ICARS when ataxia disease stages and Barthel index were used as external criteria and the redundant and overlapping nature of several items gave rise to a considerable number of contradictory ratings.
Inter‐rater reliability of the International Cooperative Ataxia Rating Scale (ICARS)
TLDR
The ICARS exhibits very high inter‐rater reliability even without prior observer standardisation and is sensitive to a range of ataxia severities from very mild to severe.
Unified Huntington's disease rating scale: reliability and consistency
TLDR
The limited longitudinal database indicates that the UHDRS may be useful for tracking changes in the clinical features of HD over time and there was an excellent degree of interrater reliability for the motor scores.
Quantitative measures of neurological function in chronic neuromuscular diseases and ataxia
Measuring Friedreich ataxia: Interrater reliability of a neurologic rating scale
TLDR
The authors discuss the problems related to rating scales in the ataxias, report a neurologic rating scale for FA, and demonstrate acceptable interrater reliability of the instrument.
The natural history of degenerative ataxia: a retrospective study in 466 patients.
TLDR
In FRDA, the time until confinement to wheelchair was shorter in patients with earlier disease onset, suggesting that patients with long GAA repeats and early disease onset have a poor prognosis, and in MSA, later age of onset increased the risk of rapid progression and death.
Idiopathic cerebellar ataxia of late onset: natural history and MRI morphology.
TLDR
The majority of the patients with additional non-cerebellar symptoms had evidence of an atrophy of the cerebellum and the brainstem suggesting the presence of olivo-ponto-ceebellar atrophy (OPCA), however, MRI morphology was not compatible with the diagnosis of OPCA.
Spinocerebellar ataxia type 6: genotype and phenotype in German kindreds
TLDR
This study provides the first detailed characterisation of the SCA6 phenotype, an autosomal dominant cerebellar ataxia of which the mutation causing the disease has recently been characterised as an expanded CAG trinucleotide repeat in the gene coding for the α1A-subunit of the voltage dependent calcium channel.
Mitral valve replacement.
  • S. Attar
  • Medicine
    Maryland state medical journal
  • 1965
...
...