Scale for the assessment and rating of ataxia

  title={Scale for the assessment and rating of ataxia},
  author={Tanja Schmitz-H{\"u}bsch and Sophie T{\'e}zenas du Montcel and L{\'a}szl{\'o} Balik{\'o} and Jos{\'e} Berciano and Sylvia Boesch and Chantal Depondt and Paola Giunti and Christoph Globas and Jon Infante and J. S. Kang and B Kremer and Caterina Mariotti and B{\'e}la Melegh and Massimo Pandolfo and Maryla Rakowicz and Pascale Ribai and Rafał Rola and L. Sch{\"o}ls and Sandra Szymanski and Bart P.C. Van de Warrenburg and Alexandra D{\"u}rr and Thomas Klockgether},
  pages={1717 - 1720}
Objective: To develop a reliable and valid clinical scale measuring the severity of ataxia. Methods: The authors devised the Scale for the Assessment and Rating of Ataxia (SARA) and tested it in two trials of 167 and 119 patients with spinocerebellar ataxia. Results: The mean time to administer SARA in patients was 14.2 ± 7.5 minutes (range 5 to 40). Interrater reliability was high, with an intraclass coefficient (ICC) of 0.98. Test-retest reliability was high with an ICC of 0.90. Internal… 

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