Scale for the assessment and rating of ataxia

@article{SchmitzHbsch2006ScaleFT,
  title={Scale for the assessment and rating of ataxia},
  author={Tanja Schmitz-H{\"u}bsch and Sophie T{\'e}zenas du Montcel and L{\'a}szl{\'o} Balik{\'o} and Jos{\'e} Berciano and Sylvia Boesch and Chantal Depondt and Paola Giunti and Christoph Globas and Jon Infante and J. S. Kang and B Kremer and Caterina Mariotti and B{\'e}la Melegh and Massimo Pandolfo and Maryla Rakowicz and Pascale Ribai and Rafał Rola and L. Sch{\"o}ls and Sandra Szymanski and Bart P.C. Van de Warrenburg and Alexandra D{\"u}rr and Thomas Klockgether},
  journal={Neurology},
  year={2006},
  volume={66},
  pages={1717 - 1720}
}
Objective: To develop a reliable and valid clinical scale measuring the severity of ataxia. Methods: The authors devised the Scale for the Assessment and Rating of Ataxia (SARA) and tested it in two trials of 167 and 119 patients with spinocerebellar ataxia. Results: The mean time to administer SARA in patients was 14.2 ± 7.5 minutes (range 5 to 40). Interrater reliability was high, with an intraclass coefficient (ICC) of 0.98. Test-retest reliability was high with an ICC of 0.90. Internal… 
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Usefulness of the Scale for Assessment and Rating of Ataxia (SARA)
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A non-linear relationship between SARA scores and age was found and the scale should never be used with non-impaired children, and the authors were unable to calculate scores for speech, due to the low variance in the range.
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The Turkish-language adaptation of the Brief Ataxia Rating Scale is reliable and valid for application in children and will contribute to broadening its use in the pediatric age group in particular.
Commentary on the Paper “Progression of Gait Ataxia in Patients with Degenerative Cerebellar Disorders: a 4-Year Follow-Up Study”
TLDR
Findings imply that the SARA scores could be also presented using a multiplication factor of 2.5, which could make the results more readable when presented in a range from 0 to 100 than when presented from0 to 40, both in figures and tables.
Application of a Scale for the Assessment and Rating of Ataxia (SARA) in Friedreich's ataxia patients according to posturography is limited
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SARA is a complementary tool for evaluation of the severity of ataxia in mild stroke patients with features of posterior circulation with significant value for prediction of mRS at discharge.
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The EQ-5D visual analogue scale proved insufficient for longitudinal assessment, but validly reflected patients' impression of change, and the clinical relevance of SCAFI and 9-hole pegboard score changes warrants further exploration.
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