Rett's syndrome: prevalence and impact on progressive severe mental retardation in girls.

@article{Hagberg1985RettsSP,
  title={Rett's syndrome: prevalence and impact on progressive severe mental retardation in girls.},
  author={Bengt Hagberg},
  journal={Acta paediatrica Scandinavica},
  year={1985},
  volume={74 3},
  pages={405-8}
}
The prevalence of Rett's syndrome was studied in a part of southwestern Sweden comprising five counties and the city of Gothenburg. In a population of 315469 children and adolescents, 6-17 years of age, 10 cases were detected, all girls. The corresponding prevalence was 0.65/10 000 girls, i.e. about twice that of phenylketonuria (PKU) in the same area. As… CONTINUE READING