Respiratory muscle dysfunction in facioscapulohumeral muscular dystrophy.

Abstract

Respiratory insufficiency in facioscapulohumeral muscular dystrophy has rarely been studied. We compared two age- and sex-matched groups of 29 patients, with and without respiratory dysfunction. Tests in the 29 patients with respiratory dysfunction suggested predominant expiratory muscle dysfunction, leading to ineffective cough in 17 patients. Supine and… (More)
DOI: 10.1016/j.nmd.2015.04.011

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