Reliability and validity of the International Cooperative Ataxia Rating Scale: A study in 156 spinocerebellar ataxia patients

@article{SchmitzHbsch2006ReliabilityAV,
  title={Reliability and validity of the International Cooperative Ataxia Rating Scale: A study in 156 spinocerebellar ataxia patients},
  author={Tanja Schmitz-H{\"u}bsch and Sophie Tezenas du Montcel and L{\'a}szl{\'o} Balik{\'o} and Sylvia Boesch and Sara Bonato and Roberto Fancellu and Paola Giunti and Christoph Globas and Jun-Suk Kang and B Kremer and Caterina Mariotti and B{\'e}la Melegh and Maryla Rakowicz and Rafał Rola and Sylvie Romano and L. Sch{\"o}ls and Sandra Szymanski and Bart P.C. Van de Warrenburg and Elzbieta Zdzienicka and Alexandra D{\"u}rr and Thomas Klockgether},
  journal={Movement Disorders},
  year={2006},
  volume={21}
}
To evaluate the efficacy of treatments in spinocerebellar ataxias (SCAs), appropriate clinical scales are required. This study evaluated metric properties of the International Cooperative Ataxia Rating Scale (ICARS) in 156 SCA patients and 8 controls. ICARS was found to be a reliable scale satisfying accepted criteria for interrater reliability, test–retest reliability, and internal consistency. Although validity testing was limited, we found evidence of validity of ICARS when ataxia disease… 
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