Reliability and validity of the International Cooperative Ataxia Rating Scale: A study in 156 spinocerebellar ataxia patients

@article{SchmitzHbsch2006ReliabilityAV,
  title={Reliability and validity of the International Cooperative Ataxia Rating Scale: A study in 156 spinocerebellar ataxia patients},
  author={Tanja Schmitz-H{\"u}bsch and Sophie Tezenas du Montcel and L{\'a}szl{\'o} Balik{\'o} and Sylvia Boesch and Sara Bonato and Roberto Fancellu and Paola Giunti and Christoph Globas and Jun-Suk Kang and B Kremer and Caterina Mariotti and B{\'e}la Melegh and Maryla Rakowicz and Rafał Rola and Sylvie Romano and L. Sch{\"o}ls and Sandra Szymanski and Bart P.C. Van de Warrenburg and Elzbieta Zdzienicka and Alexandra D{\"u}rr and Thomas Klockgether},
  journal={Movement Disorders},
  year={2006},
  volume={21}
}
To evaluate the efficacy of treatments in spinocerebellar ataxias (SCAs), appropriate clinical scales are required. This study evaluated metric properties of the International Cooperative Ataxia Rating Scale (ICARS) in 156 SCA patients and 8 controls. ICARS was found to be a reliable scale satisfying accepted criteria for interrater reliability, test–retest reliability, and internal consistency. Although validity testing was limited, we found evidence of validity of ICARS when ataxia disease… 
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Reliability and validity of the scale for the assessment and rating of ataxia: A study in 64 ataxia patients
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The results suggest that SARA is a reliable and valid measure of ataxia in non‐SCA ataxian patients and is closely correlated with disease duration.
The international cooperative ataxia rating scale in Machado‐Joseph disease. Comparison with the unified multiple system atrophy rating scale
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It is concluded that the total ICARS score is a reliable method for longitudinal evaluation of ataxia in MJD, but a disease specific scale should be developed.
Reliability and validity of ICARS in focal cerebellar lesions
  • B. Schoch, J. Regel, D. Timmann
  • Psychology, Medicine
    Movement disorders : official journal of the Movement Disorder Society
  • 2007
TLDR
Reliability and validity of the semiquantitative International Cooperative Ataxia Rating Scale (ICARS) has recently been examined in patients with degenerative ataxias for the first time and an excellent Cronbach's α as a measurement for internal consistency was found.
Multiple Sclerosis and Related Disorders
TLDR
Investigating the reliability and validity of the Turkish version of the International Cooperative Ataxia Rating Scale (ICARS) and Scale for the Assessment and Rating of AtaxIA (SARA) demonstrated that ICARS and SARA are both reliable in MS patients with ataxia.
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TLDR
The Scale for the Assessment and Rating of Ataxia is a reliable and valid measure of ataxia, making it an appropriate primary outcome measure for clinical trials.
Development of a brief ataxia rating scale (BARS) based on a modified form of the ICARS
TLDR
A brief ataxia rating scale (BARS) for use by movement disorder specialists and general neurologists is developed, valid, reliable, and sufficiently fast and accurate for clinical purposes.
Usefulness of the Scale for Assessment and Rating of Ataxia (SARA)
Cross-cultural adaptation and validation of the International Cooperative Ataxia Rating Scale (ICARS) to Brazilian Portuguese.
TLDR
The present ICARS version is adapted for the Brazilian culture and can be used to assess ataxic patients and showed good validity of the construct and high internal consistency for the full scale, except for the oculomotor domain.
Comparison of three clinical rating scales in Friedreich ataxia (FRDA)
TLDR
Although originally developed for the use in dominantly inherited ataxias, SARA can also be used successfully to assess afferent ataxia, which is the predominant form in FRDA and is well suited forclinical trials of FRDA.
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