Relative survival of childhood and adult medulloblastomas and primitive neuroectodermal tumors (PNETs)

@article{Smoll2012RelativeSO,
  title={Relative survival of childhood and adult medulloblastomas and primitive neuroectodermal tumors (PNETs)},
  author={Nicolas Roydon Smoll},
  journal={Cancer},
  year={2012},
  volume={118}
}
  • N. Smoll
  • Published 1 March 2012
  • Medicine
  • Cancer
Medulloblastomas are 1 of the most common brain tumors in children but can affect individuals of all ages. For this report, the author investigated the impact of medulloblastomas/primitive neuroectodermal tumors (PNETs) on the US population with a focus on age differences. 

Suprasellar Primitive Neuroectodermal Tumor in an Adult.

A 31-year-old woman with bilateral vision loss and a bitemporal hemianopia is diagnosed with primitive neuroectodermal tumors, and neuroimaging revealed a suprasellar mass, and pathology was consistent with PNET.

Medulloblastomas: Survival Differences Between Children and Adults

Up to 4 years post-diagnosis, the prognosis remains the same, but between 4 and 10 years of follow-up, adults become significantly more likely to die than children.

Primitive Neuroectodermal Tumor, a Rare Cause of Musculoskeletal Manifestations in a Child

Among small blue round cell tumors, primitive neuroectodermal tumors (PNETs) are a group of Ewing sarcoma family of tumors that are highly aggressive, poorly differentiated and form a group of tumors

Primitive neuroectodermal tumors of the abdominal wall and vulva in children: Report of two cases and review of the literature

PNET is a rare, fast-growing, highly malignant tumor that requires histologic and molecular analyses for exact diagnosis, and multimodal treatment is required to achieve a good prognosis.

Adult Medulloblastoma: Updates on Current Management and Future Perspectives

The state of the art for adult medulloblastoma diagnosis and treatment is reviewed, presenting novel molecular advances and their therapeutic implications and discussing the central role of hub centers to guarantee the highest quality of care and a better overall outcome for this rare tumor.

Epidemiology of childhood brain tumors

This chapter reviews the descriptive and analytic epidemiology of childhood brain tumors, including a discussion of the roles of radiation exposure, established predisposing syndromes, and other suspected risk factors.

Incidence, Trends, and Survival of Children With Embryonal Tumors

A comprehensive overview of pediatric embryonal tumors from a well-established, complete nationwide cancer registry is presented, finding significant increasing trend for hepatoblastomas was detected for the first time in Europe.

Posterior Fossa Tumors in Adult Patients.

The incidence of medulloblastomas and primitive neurectodermal tumours in adults and children

...

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