Pulmonary lymphangioleiomyomatosis: high-resolution CT findings in four cases.

  title={Pulmonary lymphangioleiomyomatosis: high-resolution CT findings in four cases.},
  author={Daniel C Rappaport and Gordon L. Weisbrod and Stephen J. Herman and Dean W. Chamberlain},
  journal={AJR. American journal of roentgenology},
  volume={152 5},
Lymphangioleiomyomatosis is a rare disease of unknown cause that affects women of reproductive age. It is characterized by progressive proliferation of smooth muscle in the lung. The patients present with progressive shortness of breath, pneumothorax, chylous effusion, and hemoptysis. Four patients with biopsy-proved lymphangioleiomyomatosis of the lung were evaluated using high-resolution CT. In all patients, the scan showed well-defined cystic air spaces, surrounded by uniformly thin walls… CONTINUE READING


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