Pulmonary lymphangioleiomyomatosis: a report of 46 patients including a clinicopathologic study of prognostic factors.

@article{Kitaichi1995PulmonaryLA,
  title={Pulmonary lymphangioleiomyomatosis: a report of 46 patients including a clinicopathologic study of prognostic factors.},
  author={Masanori Kitaichi and Kousuke Nishimura and Harumi Itoh and Takateru Izumi},
  journal={American journal of respiratory and critical care medicine},
  year={1995},
  volume={151 2 Pt 1},
  pages={527-33}
}
The clinical and pathologic features of 46 patients from Japan, Korea, and Taiwan with pulmonary lymphangioleiomyomatosis (LAM) were studied. Only two (5%) among 40 evaluable treatments were assessed to be effective. Some prognostic factors of LAM were recognized. A reduction of the forced expiratory volume in one second/forced vital capacity (FEV1/FVC) ratio was a poor prognostic factor at 2 yr after the first examination, with a statistically significant difference (p < 0.05). An increase in… CONTINUE READING