Pulmonary hypertension and other potentially fatal pulmonary complications in systemic juvenile idiopathic arthritis.

@article{Kimura2013PulmonaryHA,
  title={Pulmonary hypertension and other potentially fatal pulmonary complications in systemic juvenile idiopathic arthritis.},
  author={Yukiko Kimura and Jennifer E. Weiss and Kathryn L Haroldson and Tzielan C Lee and Marilynn Punaro and Sheila Freires de Oliveira and Egla Rabinovich and Meredith P Riebschleger and Jordi Ant{\'o}n and Peter R. Blier and Valeria Maria Gerloni and Melissa M Hazen and Elizabeth Kessler and Karen Onel and Murray H. Passo and Robert M. Rennebohm and Carol A. Wallace and Patricia Woo and Nico Martinus Wulffraat},
  journal={Arthritis care & research},
  year={2013},
  volume={65 5},
  pages={745-52}
}
OBJECTIVE Systemic juvenile idiopathic arthritis (JIA) is characterized by fevers, rash, and arthritis, for which interleukin-1 (IL-1) and IL-6 inhibitors appear to be effective treatments. Pulmonary arterial hypertension (PAH), interstitial lung disease (ILD), and alveolar proteinosis (AP) have recently been reported with increased frequency in systemic JIA patients. Our aim was to characterize and compare systemic JIA patients with these complications to a larger cohort of systemic JIA… CONTINUE READING