Psychopathology in Williams Syndrome: The Effect of Individual Differences Across the Life Span

@article{Dodd2009PsychopathologyIW,
  title={Psychopathology in Williams Syndrome: The Effect of Individual Differences Across the Life Span},
  author={Helen F. Dodd and Melanie Porter},
  journal={Journal of Mental Health Research in Intellectual Disabilities},
  year={2009},
  volume={2},
  pages={109 - 89}
}
  • H. Dodd, M. Porter
  • Published 2009
  • Psychology
  • Journal of Mental Health Research in Intellectual Disabilities
This research aimed to comprehensively explore psychopathology in Williams syndrome (WS) across the life span and evaluate the relationship between psychopathology and age category (child or adult), gender, and cognitive ability. The parents of 50 participants with WS, ages 6–50 years, were interviewed using the Schedule for Affective Disorders and Schizophrenia for School-Age Children. The prevalence of a wide range of Axis I Diagnostic and Statistical Manual of Mental Disorders (DSM-IV… Expand
The Interplay Between Anxiety and Social Functioning in Williams Syndrome
TLDR
Severity of anxiety was correlated with a greater degree of social dysfunction as measured by the SRS in this group and the profile of social skills for the two groups differed in their social abilities. Expand
Psychopathology and behavior problems in children and adolescents with Williams syndrome: Distinctive relationships with cognition
TLDR
In the children, higher IQ scores were found to be significantly associated with less externalizing problems, while in the adolescents cognitive abilities were found with less internalizing symptoms, providing further insight into the links between psychopathology and behavior problems and cognitive abilities in WS. Expand
Longitudinal course of anxiety in children and adolescents with Williams syndrome
TLDR
There was a significant relation between executive functioning and anxiety such that the presence of an anxiety diagnosis was associated with increased scores on behavioral regulation, indicative of increased difficulty with inhibitory control of affect and behavior. Expand
The Profiles and Correlates of Psychopathology in Adolescents and Adults with Williams, Fragile X and Prader–Willi Syndromes
TLDR
Dissociations in the potential risk markers of psychopathology between genetic syndromes are highlighted and implications for intervention are discussed. Expand
Detecting Psychiatric Profile in Genetic Syndromes: A Comparison of Down Syndrome and Williams Syndrome
TLDR
Results indicate that the genetic etiology of ID differently affects the psychiatric characteristics of the groups and suggest the importance of a targeted psychiatric care for individuals with WS and DS. Expand
The Interplay Between Anxiety and Social Functioning in Williams Syndrome
The developmental disorder Williams syn- drome (WS) has been associated with an atypical social profile of hyper-sociability and heightened social sensitiv- ity across the developmental spectrum. InExpand
Anxiety characteristics in individuals with Williams syndrome.
TLDR
The utility of a formulation framework to explore anxiety characteristics in atypical populations and has outlined new avenues for research are demonstrated. Expand
Examining reports of mental health in adults with Williams syndrome.
TLDR
The adults with WS provided reliable information regarding their mental health, thus providing further evidence that anxiety is part of the behavioural phenotype of the syndrome. Expand
Predictors of specific phobia in children with Williams syndrome.
TLDR
Children with behaviour regulation difficulties in or just below the clinical range were at the greatest risk of developing Specific phobia, and the importance of evaluating for nonlinear effects to provide accurate model specification when characterising relations among a dependent variable and possible predictors is highlighted. Expand
Behavioural features of Italian infants and young adults with Williams-Beuren syndrome.
TLDR
The data could support the existence of some 'intrinsic' behavioural characteristics in Williams-Beuren syndrome such as inattention and anxiety, which are detectable and important at any age; both learning and social exposure to a structured context such as school could help diminish self-absorbed behaviour. Expand
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