Pseudomyxoma peritonei: the 'controversial' disease.

  title={Pseudomyxoma peritonei: the 'controversial' disease.},
  author={Eleni Galani and Gavin M. Marx and Christopher B Steer and Giuseppe Culora and Peter G. Harper},
  journal={International journal of gynecological cancer : official journal of the International Gynecological Cancer Society},
  volume={13 4},
Pseudomyxoma peritonei (PMP) is a rare disease that is characterized by a large amount of mucinous ascites with peritoneal and omental implants. The etiology of the disease remains unclear. Histologically, two main categories have been described: disseminated peritoneal adenomucinosis (DPAM) and peritoneal mucinous carcinomatosis (PMCA). It is commonly diagnosed incidentally at laparotomy. Most investigators agree that radical surgical debulking and appendectomy are the cornerstone of treatment… CONTINUE READING