Proposal for a new clinical entity, IgG4-positive multiorgan lymphoproliferative syndrome: analysis of 64 cases of IgG4-related disorders.

@article{Masaki2009ProposalFA,
  title={Proposal for a new clinical entity, IgG4-positive multiorgan lymphoproliferative syndrome: analysis of 64 cases of IgG4-related disorders.},
  author={Yasufumi Masaki and Ling-yi Dong and Nozomu Kurose and Koichi Kitagawa and Yukihiko Morikawa and Michiko Yamamoto and Hiroyuki Takahashi and Yasuhisa Shinomura and Kazuho Imai and Toshiaki Saeki and Atsushi Azumi and Shinji Nakada and Eitaro Sugiyama and Shoji Matsui and Tomoki Origuchi and Sumusu Nishiyama and Isao Nishimori and Takaki Nojima and Kinya Yamada and Mitsuhiro Kawano and Yoh Zen and Mayumi Kaneko and Kana Miyazaki and Kazuo Tsubota and Katsumi Eguchi and Koichi Tomoda and Toshioki Sawaki and Takako Kawanami and Michi Tanaka and Toshihiro Fukushima and Susumu Sugai and Hisanori Umehara},
  journal={Annals of the rheumatic diseases},
  year={2009},
  volume={68 8},
  pages={1310-5}
}
BACKGROUND Mikulicz's disease (MD) has been considered as one manifestation of Sjögren's syndrome (SS). Recently, it has also been considered as an IgG(4)-related disorder. OBJECTIVE To determine the differences between IgG(4)-related disorders including MD and SS. METHODS A study was undertaken to investigate patients with MD and IgG(4)-related disorders registered in Japan and to set up provisional criteria for the new clinical entity IgG(4)-positive multiorgan lymphoproliferative… CONTINUE READING