Prolonged moderate-intensity exercise without and with L-carnitine supplementation in patients with MCAD deficiency


Medium-chain acyl-CoA dehydrogenase deficiency (MCADD) is probably the most common inborn error of fatty acid oxidation (FAO). Routine L-carnitine supplementation in the treatment of MCADD is controversial. To establish the effects of L-carnitine supplementation during prolonged moderate-intensity exercise in MCADD, five patients and three control subjects… (More)
DOI: 10.1007/s10545-006-0355-3


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