Progression of Hip Dysplasia in Mucopolysaccharidosis Type I Hurler After Successful Hematopoietic Stem Cell Transplantation.

@article{Langereis2016ProgressionOH,
  title={Progression of Hip Dysplasia in Mucopolysaccharidosis Type I Hurler After Successful Hematopoietic Stem Cell Transplantation.},
  author={E. Langereis and Matthijs M den Os and C. Breen and S. Jones and O. Knaven and Jean Mercer and W. Miller and P. Kelly and Jim Kennedy and T. Ketterl and A. O'meara and P. Orchard and T. Lund and R. V. van Rijn and R. Sakkers and K. White and F. Wijburg},
  journal={The Journal of bone and joint surgery. American volume},
  year={2016},
  volume={98 5},
  pages={
          386-95
        }
}
  • E. Langereis, Matthijs M den Os, +14 authors F. Wijburg
  • Published 2016
  • Medicine
  • The Journal of bone and joint surgery. American volume
  • BACKGROUND Dysostosis multiplex contributes substantially to morbidity in patients with Hurler syndrome (mucopolysaccharidosis type I Hurler phenotype [MPS I-H]), even after successful hematopoietic stem cell transplantation (HSCT). One of the hallmarks of dysostosis multiplex in MPS I-H is hip dysplasia, which often requires surgical intervention. We sought to describe in detail the course of hip dysplasia in this group of patients, as assessed by radiographic analysis, and to identify… CONTINUE READING
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