Prognostic significance of histopathologic subsets in idiopathic pulmonary fibrosis.

@article{Bjoraker1998PrognosticSO,
  title={Prognostic significance of histopathologic subsets in idiopathic pulmonary fibrosis.},
  author={J A Bjoraker and Jeong Ha Ryu and M Edwin and Jeffrey L Myers and Henry D. Tazelaar and Darrell Schroeder and Kenneth P. Offord},
  journal={American journal of respiratory and critical care medicine},
  year={1998},
  volume={157 1},
  pages={
          199-203
        }
}
Idiopathic pulmonary fibrosis (IPF) is a generally fatal disorder with a reported median survival of 3 to 6 yr. This has been based on relatively few studies with diagnoses inconsistently confirmed by adequate lung biopsy. Retrospective analysis of 104 patients with IPF who had open lung biopsy (OLB) at Mayo Medical Center from 1976 to 1985 was performed to establish the overall survival rate, the spectrum of histopathological subgroups and their associated prognostic significance. The study… Expand

Paper Mentions

Interventional Clinical Trial
Idiopathic pulmonary fibrosis (IPF), a chronic fibrotic lung disease of unknown cause, is characterized by relentless progression, with a three-year mortality of up to 50%. IPF has… Expand
ConditionsIdiopathic Pulmonary Fibrosis
InterventionOther
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