Primary pulmonary lymphangiectasia in infancy and childhood.

  title={Primary pulmonary lymphangiectasia in infancy and childhood.},
  author={Pierre M. Barker and Charles R Esther and Lynn Ansley Fordham and Susan J Maygarden and William K. Funkhouser},
  journal={The European respiratory journal},
  volume={24 3},
Primary pulmonary lymphangiectasia (PPL) is a rare disorder of unknown aetiology characterised by dilatation of the pulmonary lymphatics. PPL is widely reported to have a poor prognosis in the neonatal period and little is known about the clinical features of patients who survive the newborn period. The current authors report the outcome in nine patients diagnosed in infancy with PPL over a 15-yr period at a single university-based hospital clinic and followed for a median of 6 yrs. Although… CONTINUE READING
15 Extracted Citations
27 Extracted References
Similar Papers

Citing Papers

Publications influenced by this paper.
Showing 1-10 of 15 extracted citations

Referenced Papers

Publications referenced by this paper.
Showing 1-10 of 27 references

Congenital malformations of the lungs and airways

  • BS Clements
  • St Louis, Mosby,
  • 1999

Congential malformations of the lower respiratory tract

  • T. Krummel
  • Respiratory disorders in the newborn
  • 1998

Similar Papers

Loading similar papers…