Primary pulmonary lymphangiectasia in infancy and childhood.

@article{Barker2004PrimaryPL,
  title={Primary pulmonary lymphangiectasia in infancy and childhood.},
  author={Pierre M. Barker and Charles R Esther and Lynn Ansley Fordham and Susan J Maygarden and William K. Funkhouser},
  journal={The European respiratory journal},
  year={2004},
  volume={24 3},
  pages={413-9}
}
Primary pulmonary lymphangiectasia (PPL) is a rare disorder of unknown aetiology characterised by dilatation of the pulmonary lymphatics. PPL is widely reported to have a poor prognosis in the neonatal period and little is known about the clinical features of patients who survive the newborn period. The current authors report the outcome in nine patients diagnosed in infancy with PPL over a 15-yr period at a single university-based hospital clinic and followed for a median of 6 yrs. Although… CONTINUE READING
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