Clinical, radiological and histological aspects of a case of primary bone haemangiopericytoma, treated by wide surgical resection and pre- and postoperative radiotherapy, are described. The patient was disease-free 20 months from the operation. From a literature review of 52 cases of this very rare tumour it emerges that the tumour is aggressive but of variable malignancy. Prognosis seems to depend on histology, size at diagnosis and treatment. The best available treatment is probably wide exeresis plus radiotherapy.