Extraskeletal osteosarcoma (EOS) is a rare entity. Most human cases have been described in the soft tissues of the limb. Primary hepatic osteosarcoma is extremely uncommon with only seven cases reported in the world’s literature. Of these cases, no patient survived more than 8 weeks from the time of diagnosis. We describe a young patient with a symptomatic primary hepatic osteosarcoma that was successfully treated by surgical resection and adjuvant chemotherapy. She is alive and tumor free 3 years after surgery.