Primary Ewing Sarcoma of the Kidney with Inferior Vena Cava Invasion

@article{Nam2015PrimaryES,
  title={Primary Ewing Sarcoma of the Kidney with Inferior Vena Cava Invasion},
  author={Jong Kil Nam},
  journal={Medical \& Surgical Urology},
  year={2015},
  volume={4},
  pages={1-3}
}
  • J. Nam
  • Published 2015
  • Medicine
  • Medical & Surgical Urology
Ewing sarcoma is typically a skeletal based tumor of presumed neuroectodermal origin. Primary Ewing sarcoma of the kidney is exceedingly rare and is usually found in young adults. We report a case of primary Ewing sarcoma with inferior vena cava (IVC) invasion that was managed successfully with radical nephrectomy and partial replacement of IVC using bovine pericardial patch. 
1 Citations
Primary Renal Ewing Sarcoma: A Case Report and Review of the Literature.
TLDR
The case of a 22-year-old male with primary Ewing sarcoma/primitive neuroectodermal tumor (EWS/PNET) of the kidney who underwent right radical nephrectomy and adjuvant chemo-radiation is presented. Expand

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  • Figure 3: (A) The resected inferior vena cava showed invasive sarcoma (H&E, x40). (B) The tumor cells have round and hyperchromatic nuclei and show rossetoid arrangement (H&E, x400). Figure 4: The tumor cells showing strong membranous immunoreactivity for CD99 (x200). Citation: Nam JK
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