Prevalence of auditory neuropathy spectrum disorder in an auditory health care service.

@article{Penido2013PrevalenceOA,
  title={Prevalence of auditory neuropathy spectrum disorder in an auditory health care service.},
  author={R. C. Penido and M. Isaac},
  journal={Brazilian journal of otorhinolaryngology},
  year={2013},
  volume={79 4},
  pages={
          429-33
        }
}
UNLABELLED Auditory neuropathy spectrum disorder (ANSD) is characterized by impairment of the auditory nerve associated with preservation of outer hair cell function. OBJECTIVE To establish the prevalence of ANSD in subjects with sensorineural hearing loss (SNHL). METHOD This retrospective study was carried out between 2010 and 2012 and included the charts of 2,292 individuals with SNHL. Data from otolaryngological and audiological examinations based on pure-tone and speech audiometry… Expand
Auditory Neuropathy : Clinical Evaluation and Diagnostic Approach Neuropatia Auditiva
Introduction: Auditory neuropathy is a condition in which there is a change in the neuronal transmission of the auditory stimuli. Our objective was to describe the patients’ series within theExpand
Molecular study of patients with auditory neuropathy.
TLDR
The present study aimed to investigate molecular changes in the OTOF gene in patients with auditory neuropathy, and to develop a DNA chip for the molecular diagnosis of auditory Neuropathy using mass spectrometry for genotyping. Expand
Study of cochlear microphonic potentials in auditory neuropathy.
TLDR
The presence of the Cochlear Microphonic is a determining finding in the differential diagnosis of Auditory Neuropathy/Dyssynchrony. Expand
Performance of Cochlear Implants in Pediatric Patients with Auditory Neuropathy Spectrum Disorder.
TLDR
The comparison of hearing levels before and after CI use showed a significant improvement in all patients, with p<0.05, and individuals with an demonstrated a significant gain in hearing levels and language use with CI. Expand
The Prevalence and Causes of Auditory Neuropathy/Dys-synchrony (AN/AD) in Children with Hearing Impairment
TLDR
The findings of this study showed that there are the relationships between AN/AD and fluctuating hearing loss, acoustic reflex, high bilirubin, blood exchange after birth, neonatal intensive (NICU) care unit (P < 0.05). Expand
Relationship Between Patients with Clinical Auditory Neuropathy Spectrum Disorder and Mutations in Gjb2 Gene
TLDR
It is found that there is no relationship between patients with clinical auditory neuropathy spectrum disorder and mutations in GJB2 gene (p>0.05). Expand
Relationship Between Patients with Clinical Auditory Neuropathy Spectrum Disorder and Mutations in Gjb2 Gene
TLDR
The pattern of clinical relationship between patients with clinical diagnosis with auditory neuropathy spectrum disorder and mutations in GJB2 gene was analyzed and it was found no relationship was found. Expand
Auditory synaptopathy, auditory neuropathy, and cochlear implantation
TLDR
A nuanced molecular classification of ANSD is put forth that has implications for preoperative counseling for patients with this disorder prior to cochlear implantation and is based on the molecular site of lesion typically derived from genetic evaluation (synaptopathy vs. neuropathy). Expand
Molecular approach of auditory neuropathy.
TLDR
There are differences at the molecular level in patients with and without auditory neuropathy. Expand
Agreement/disagreement between caloric and video head impulse tests: does it reveal something? Report from three individuals with auditory neuropathy spectrum disorder
TLDR
The caloric responses were found to be hypofunctional in all three participants suggesting vestibular deficits, suggesting that in addition to the auditory system, the Vestibular system may also be affected in ANSD. Expand
...
1
2
3
...

References

SHOWING 1-10 OF 34 REFERENCES
Auditory neuropathy spectrum disorder: its prevalence and audiological characteristics in an Indian tertiary care hospital.
TLDR
The prevalence of ANSD in India is 5.3% and in children diagnosed with severe to profound hearing loss is 14%. Expand
Audiological Results in a Group of Children with Auditory Neuropathy Spectrum Disorder
TLDR
Absent or severely abnormal ABR along with present CMs are the most reliable measures for detecting this disorder at this stage. Expand
Prevalence and risk factors for auditory neuropathy spectrum disorder in a screened newborn population at risk for hearing loss.
TLDR
Auditory Neuropathy Spectrum Disorder is not an extremely rare hearing disorder and Screening for hearing loss via OAEs, MEMR and ABR examinations concurrently are essential for the accurate diagnosis of ANSD. Expand
The prevalence of auditory neuropathy in students with hearing impairment in Tehran, Iran.
TLDR
It is suggested that a complete panel of audiological tests for detection of auditory neuropathy be performed before admission of students with hearing impairment to schools. Expand
The Varieties of Auditory Neuropathy
TLDR
Patients with audiological and neurophysiological criteria for hearing loss due to auditory neuropathy are described, and analyses of the clinical features indicate that auditory neuropathies vary in several measures including age of onset, presence of peripheral neuropathy, etiology, and behavioral and physiological measures of auditory function. Expand
Auditory neuropathy.
TLDR
It is suggested that this type of hearing impairment is due to a disorder of auditory nerve function and may have, as one of its causes, a neuropathy of the auditory nerve, occurring either in isolation or as part of a generalized neuropathic process. Expand
Prevalence of auditory neuropathy/synaptopathy in a population of children with profound hearing loss.
TLDR
This study shows that AN/AS is a common finding in the population of hearing impaired infants, and clinicians and other health care professionals should generally be sensitised forAN/AS in infants, so that an appropriate treatment can promptly be initiated. Expand
Speech perception and cortical auditory evoked potentials in cochlear implant users with auditory neuropathy spectrum disorders.
TLDR
In children with ANSD using cochlear implants, the P(1) component can serve as a marker of central auditory cortical development and a predictor of the implanted child's speech perception performance. Expand
Clinical and audiological features in auditory neuropathy.
TLDR
Management of AN in children requires serial clinical and audiometric evaluations, with a prominent role for behavioral testing, and 9 of these 18 patients showed improvement in behavioral thresholds over time, indicating that a subset of children with AN may recover useful hearing levels. Expand
Prevalence of auditory neuropathy (AN) among infants and young children with severe to profound hearing loss.
TLDR
This study aimed to detect its prevalence among infants and young children with severe to profound hearing loss and found 15 patients were found to have auditory neuropathy according to the criteria for diagnosis. Expand
...
1
2
3
4
...