Pressure-support ventilation in a child with merosin-deficient congenital muscular dystrophy under sevoflurane anesthesia.

@article{Prgardien2016PressuresupportVI,
  title={Pressure-support ventilation in a child with merosin-deficient congenital muscular dystrophy under sevoflurane anesthesia.},
  author={Caroline Pr{\'e}gardien and Th Pirotte and Francis Veyckemans},
  journal={Acta anaesthesiologica Belgica},
  year={2016},
  volume={67 3},
  pages={
          139-141
        }
}
Merosin-deficient congenital muscular dystrophy (MD-CMD) is the most common and severe form of congenital muscular dystrophy and is characterized by progressive severe hypotonia due to the absence of the merosin chain around muscle fibers. The main anesthetic concerns include a possible association with malignant hyperthermia, the risk of anesthesia-induced… CONTINUE READING