Polysplenia syndrome with agenesis of the dorsal pancreas and preduodenal portal vein presenting with obstructive jaundice--a case report and literature review.

@article{Low2011PolyspleniaSW,
  title={Polysplenia syndrome with agenesis of the dorsal pancreas and preduodenal portal vein presenting with obstructive jaundice--a case report and literature review.},
  author={Joyce Low and David M. Williams and J R Chaganti},
  journal={The British journal of radiology},
  year={2011},
  volume={84 1007},
  pages={e217-20}
}
Polysplenia, as part of the heterotaxy syndrome, is a rare embryological disorder which results from failure of development of the usual left-right asymmetry of organs. It is often associated with cardiac and biliary abnormalities, which are the usual causes of death in early neonatal life. A congenitally short pancreas and abnormalities with portal vein formation, gut malrotations and inferior vena cava anomalies are known to be associated with this rare syndrome. We report a case of… CONTINUE READING

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A rare case of heterotaxy syndrome with agenesis of the head and uncinate process of the pancreas .

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Aortic pseudocoarctation associated with polysplenia/heterotaxy syndrome.

Revista portuguesa de cardiologia : orgao oficial da Sociedade Portuguesa de Cardiologia = Portuguese journal of cardiology : an official journal of the Portuguese Society of Cardiology • 2015

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