Pleuroparenchymal fibroelastosis: report of 4 cases

  title={Pleuroparenchymal fibroelastosis: report of 4 cases},
  author={Ana Raquel Caldas Març{\^o}a and S{\'e}rgio Campainha and Carla Roberta Souza Nogueira and Filomena Costa and Agostinho Sanches and Sofia Neves},
Introduction: Pleuroparenchymal fibroelastosis (PPFE) is a rare condition characterised by predominantly upper lobe pleural and subjacent parenchymal fibrosis and elastosis. Aim: To review the cases of PPFE found in our interstitial lung disease (ILD) outpatient clinic. Methods: Patients with histological criteria of PPFE were included. Results: We included 4 patients, which are characterized in table 1. In 1 case there was another concomitant ILD. The histology was obtained by computed… CONTINUE READING