Phenylketonuria: Dietary and therapeutic challenges

@article{Giovannini2007PhenylketonuriaDA,
  title={Phenylketonuria: Dietary and therapeutic challenges},
  author={Marcello Giovannini and Elvira Verduci and Elisabetta Salvatici and Laura Fiori and Enrica Riva},
  journal={Journal of Inherited Metabolic Disease},
  year={2007},
  volume={30},
  pages={145-152}
}
PKU subjects need special attention in the definition of optimal supplementation of nutrients, which may be insufficient in relation to the type of diet and may otherwise manifest symptoms of deficit. In particular, it is necessary to pay great attention to the long-chain polyunsaturated fatty acid (LC-PUFA) levels in relation to correct development of the central nervous system. On the basis of numerous beneficial effects currently known, a permanent supplementation with LC-PUFAs, in… CONTINUE READING
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