Personality characteristics and behaviour problems in individuals of different ages with Williams syndrome

@article{Gosch1997PersonalityCA,
  title={Personality characteristics and behaviour problems in individuals of different ages with Williams syndrome},
  author={A. Gosch and R. Pankau},
  journal={Developmental Medicine \& Child Neurology},
  year={1997},
  volume={39}
}
  • A. Gosch, R. Pankau
  • Published 1997
  • Psychology, Medicine
  • Developmental Medicine & Child Neurology
To study personality characteristics and behaviour problems in different age groups more precisely, the parents of 105 children with Williams syndrome (WS) were asked to complete a questionnaire with a list of 25 personality adjectives and 18 behaviour disturbances. Three age groups – children under 10 years, adolescents between 10 and 20 years, and adults over 20 years of age – were compared. Adults with WS were described as being less lively, determined, active, restless, tearful, quarrelsome… Expand
Distinctive Personality Characteristics of 8-, 9-, and 10-Year-Olds With Williams Syndrome
TLDR
The personality profiles emerging from the CBQ and MPQ provide a crucial step toward investigations of genotype/phenotype relations. Expand
Behavioural features of Italian infants and young adults with Williams-Beuren syndrome.
TLDR
The data could support the existence of some 'intrinsic' behavioural characteristics in Williams-Beuren syndrome such as inattention and anxiety, which are detectable and important at any age; both learning and social exposure to a structured context such as school could help diminish self-absorbed behaviour. Expand
Psychopathology in Williams Syndrome: The Effect of Individual Differences Across the Life Span
This research aimed to comprehensively explore psychopathology in Williams syndrome (WS) across the life span and evaluate the relationship between psychopathology and age category (child or adult),Expand
Toward a deeper characterization of the social phenotype of Williams syndrome: The association between personality and social drive.
TLDR
Findings provide novel insight into social motivational factors underpinning the WS social behavior in real life, and suggest potential areas for behavioral intervention targeting improved social adjustment in individuals with WS. Expand
A Comparison of Behavioral and Emotional Characteristics in Children with Autism, Prader-Willi Syndrome, and Williams Syndrome
In order to investigate unique and shared characteristics and to determine factors predictive of group classification, quantitative comparisons of behavioral and emotional problems were assessedExpand
Behavioural profile and maternal stress in Greek young children with Williams syndrome.
TLDR
The consistency of the socio-emotional characteristics of children with WS across cultures and developmental stages implies a strong influence of the genetic phenotype, however, Greek mothers avoided to characterize these behaviours as pathological. Expand
Expressive language style among adolescents and adults with Williams syndrome
Language samples elicited through a picture description task were recorded from 38 adolescents and adults with Williams syndrome (WS) and one control group matched on age, and another matched on age,Expand
Can Adolescents With Williams Syndrome Tell the Difference Between Lies and Jokes?
TLDR
Almost none of the participants in any of the groups were able to correctly classify the ironic jokes, instead judging them to be lies because they did not correspond to reality. Expand
Psychopathological and Behavior Impairments in Williams-Beuren Syndrome: The Influence of Gender, Chronological Age, and Cognition
  • M. Porter, H. Dodd, D. Cairns
  • Psychology, Medicine
  • Child neuropsychology : a journal on normal and abnormal development in childhood and adolescence
  • 2009
TLDR
Gender and specific cognitive abilities related to significantly greater internalizing difficulties in Williams-Beuren syndrome, and underlying genetic and neurological differences in individuals with WBS should be explored to help explain the variability in psychopathological and cognitive functions. Expand
Evaluation of the influence of clinical symptoms on the quality of life in individuals with Williams-Beuren Syndrome
TLDR
This study identified related clinical symptoms in individuals with WBS and the impact of this disorder in their quality of life and Quality of Life Evaluation Scale (AUQEI). Expand
...
1
2
3
4
5
...

References

SHOWING 1-10 OF 29 REFERENCES
Social-emotional and behavioral adjustment in children with Williams-Beuren syndrome.
TLDR
Children with Williams-Beuren syndrome are described as showing a hypersensitivity to sounds that is more pronounced than in the control group and are found to be significantly less well-adjusted socially than the control individuals. Expand
Longitudinal study of the cognitive development in children with Williams-Beuren syndrome.
TLDR
The results suggest that the developmental outcome of children with WBS varies in specific areas of cognitive function over a 2-year period. Expand
Temperament in Williams syndrome.
TLDR
Parents of a child with Williams syndrome should be apprised of potentially negative temperament characteristics, relieved of the burden of responsibility for having a difficult child who "should" be easy, and counselled regarding the efficacy of modification of parent-child interactions with children having the difficult temperament. Expand
Hypothesis for development of a behavioral phenotype in Williams syndrome.
TLDR
Theoretical constructs from developmental behavioral genetics, attachment theory, operant conditioning, neuropsychology, and psychosocial theory considered interactively offer explanations for the characteristic behavioral phenotype of 6 factors of Williams syndrome. Expand
Adults with Williams‐Beuren syndrome: evaluation of the medical, psychological and behavioral aspects
TLDR
The adults the authors evaluated showed little disturbing behavior in comparison to other mentally retarded subjects, and achieved a good level of autonomy. Expand
Cognitive abilities and behavioural characteristics of children with idiopathic infantile hypercalcaemia.
An investigation of the psychological characteristics of 44 children aged 6-16 years with documented evidence of idiopathic infantile hypercalcaemia revealed cognitive abilities and behaviouralExpand
Head circumference of children with Williams-Beuren syndrome.
TLDR
Although head growth in WBS girls and boys was at a slower velocity, the pattern of head circumference was similar to that in the normal population. Expand
A SURVEY OF ADULTS WITH WILLIAMS SYNDROME AND IDIOPATHIC INFANTILE HYPERCALCAEMIA
  • O. Udwin
  • Psychology, Medicine
  • Developmental medicine and child neurology
  • 1990
TLDR
Comparisons between the questionnaires for the two groups revealed no phenotypical differences in their abilities or behavioural characteristics, and some caregivers were dissatisfied with the level of educational attainment, current daytime occupations and support received from professionals. Expand
Updating Norman's "Adequate Taxonomy": intelligence and personality dimensions in natural language and in questionnaires.
  • R. McCrae, P. Costa
  • Psychology, Medicine
  • Journal of personality and social psychology
  • 1985
TLDR
The relations among culture, conscientiousness, openness, and intelligence are discussed, and it is concluded that mental ability is a separate factor, though related to openness to experience. Expand
THE PSYCHOLOGICAL CHARACTERISTICS OF INFANTILE HYPERCALCEMIA: A PRELIMINARY INVESTIGATION
  • R. Arnold, W. Yule, Neil Martin
  • Medicine
  • Developmental medicine and child neurology
  • 1985
TLDR
This study clarifies some of the psychological correlates of infantile hypercalcaemia and some implications for management are suggested. Expand
...
1
2
3
...