Peroxisomal disorders in children: immunohistochemistry and neuropathology.

@article{Kamei1993PeroxisomalDI,
  title={Peroxisomal disorders in children: immunohistochemistry and neuropathology.},
  author={A. Kamei and S. Houdou and S. Takashima and Y. Suzuki and L. Becker and D. Armstrong},
  journal={The Journal of pediatrics},
  year={1993},
  volume={122 4},
  pages={
          573-9
        }
}
Immunohistochemical studies with antisera against four peroxisomal enzymes, catalase and beta-oxidation enzymes (acyl-coenzyme A oxidase, bifunctional protein, and 3-ketoacyl-CoA thiolase), were performed on brain, liver, and kidney specimens from patients with peroxisomal disorders, as well as specimens from three control subjects, by using conventional paraffin-embedded autopsy material. The patients included eight with Zellweger syndrome and one with neonatal adrenoleukodystrophy. In the… Expand
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