Perivascular cavitation of the basal ganglia in gargoylism.

@article{Norman1959PerivascularCO,
  title={Perivascular cavitation of the basal ganglia in gargoylism.},
  author={R. M. Norman and Henry Urich and N. E. France},
  journal={The Journal of mental science},
  year={1959},
  volume={105},
  pages={
          1070-7
        }
}
A case of gargoylism has been described in which the most striking pathological feature was the presence of extensive cavitation of the basal ganglia of the brain. These spaces were perivascular and differed from the small cysts commonly found in the cerebral white matter in gargoylism only in their size and localization. The patient was deaf and had no corneal opacities and there was a similarly affected male sibling. The case may therefore belong to that variant of gargoylism in which there… 
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