Perioperative management of a child with very-long-chain acyl-coenzyme A dehydrogenase deficiency.

@article{Steiner2002PerioperativeMO,
  title={Perioperative management of a child with very-long-chain acyl-coenzyme A dehydrogenase deficiency.},
  author={Luzius A. Steiner and Wolfgang Studer and E. Regula Baumgartner and Franz J. Frei},
  journal={Paediatric anaesthesia},
  year={2002},
  volume={12 2},
  pages={187-91}
}
Very-long-chain acyl-coenzyme A dehydrogenase deficiency is an inborn error of fatty acid metabolism. The clinical presentation of this disease in children is either a severe form with onset of symptoms in the first months of life, cardiomyopathy, metabolic acidosis, myopathy and a high mortality, or a less severe form manifesting mainly with hypoglycaemia… CONTINUE READING