Pentalogy of Cantrell corrected by one-stage repair.

  title={Pentalogy of Cantrell corrected by one-stage repair.},
  author={Yi-Chun Chen and H. S. Lai and Y C Duh and Jou Kou Wang and Ing-Sh Chiu},
  journal={Journal of the Formosan Medical Association = Taiwan yi zhi},
  volume={95 7},
Pentalogy of Cantrell (POC), is a rare congenital defect associated with five ventral midline abnormalities and high mortality. We report a 2,788 g female infant with partial repair of POC in the neonatal stage. This consisted of repairing the omphalocele, plicating the eventrated diaphragm and placing the heart into the thoracic cavity by fixing the pericardium to the ventral side of the diaphragm. She was well 6 months after surgery.