Pediatric Pulmonary Hypertension: Guidelines From the American Heart Association and American Thoracic Society

@article{Abman2015PediatricPH,
  title={Pediatric Pulmonary Hypertension: Guidelines From the American Heart Association and American Thoracic Society},
  author={Steven H. Abman and Georg Hansmann and Stephen L. Archer and Dunbar D. Ivy and Ian Adatia and Wendy K. Chung and Brian D. Hanna and Erika B. Rosenzweig and J. Usha Raj and David N. Cornfield and Kurt R. Stenmark and Robin H. Steinhorn and Bernard Th{\'e}baud and Jeffrey R Fineman and Titus Kuehne and Jeffrey A. Feinstein and Mark K. Friedberg and Michael G Earing and Robyn J. Barst and Roberta L. Keller and John P. Kinsella and Mary P. Mullen and Robin R. Deterding and Thomas J Kulik and George B. Mallory and Tilman Humpl and David L. Wessel},
  journal={Circulation},
  year={2015},
  volume={132},
  pages={2037–2099}
}
Pulmonary hypertension is associated with diverse cardiac, pulmonary, and systemic diseases in neonates, infants, and older children and contributes to significant morbidity and mortality. However, current approaches to caring for pediatric patients with pulmonary hypertension have been limited by the lack of consensus guidelines from experts in the field. In a joint effort from the American Heart Association and American Thoracic Society, a panel of experienced clinicians and clinician… Expand

Paper Mentions

Interventional Clinical Trial
Inhaled nitric oxide (iNO) is an effective treatment for pulmonary hypertension (PH) in term and near-term infants. Preterm infants are at risk for early PH that is associated with high… Expand
ConditionsBronchopulmonary Dysplasia, Pulmonary Hypertension
InterventionDrug
Interventional Clinical Trial
Oral L-citrulline supplementation may prevent and/or decrease the severity of chronic lung disease associated with pulmonary hypertension in preterm infants. Since oral L-citrulline… Expand
ConditionsBronchopulmonary Dysplasia, Bronchopulmonary Dysplasia Associated Pulmonary Hypertension, Chronic Lung Disease of Prematurity, (+2 more)
InterventionDietary Supplement
Executive Summary of the American Heart Association and American Thoracic Society Joint Guidelines for Pediatric Pulmonary Hypertension.
TLDR
A committee of experienced clinicians was formed to systematically identify, synthesize, and appraise relevant evidence and then to formulate evidence-based recommendations regarding the diagnosis and management of pediatric PH. Expand
A review of pediatric pulmonary hypertension with new guidelines.
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This study aims to review pediatric pulmonary hypertension by comparing the guidelines of the European Society of Cardiology (ESC), European Respiratory Society (ERS), the American Heart Association (AHA), and the European Pediatric Pulmonary Vascular Disease Network (EPPVDN). Expand
New guidelines for managing pulmonary hypertension: what the pediatrician needs to know
  • S. Abman
  • Medicine
  • Current opinion in pediatrics
  • 2016
TLDR
This review highlights a few key topics underlying guidelines for the care of children with pulmonary hypertension that are especially important for the practicing pediatrician and others, and presents some of the major recommendations from the published guidelines report. Expand
Update on pediatric pulmonary arterial hypertension
TLDR
New therapies, approved in adults and used off-label in pediatric patients, have led to improved outcomes for affected children, and advanced imaging and clinical monitoring have allowed improved risk stratification of pulmonary hypertension patients. Expand
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TLDR
This review summarizes the current understanding of pediatric pulmonary hypertension physiology, preoperative risk stratification, anesthetic risk, and intraoperative considerations relevant to the underlying pathophysiology of various forms of pulmonary hypertension. Expand
Pediatric Pulmonary Arterial Hypertension: Evaluation and Treatment
TLDR
An approach to the evaluation and management of a pediatric patient with suspected or confirmed PAH is discussed, including a series of risk stratification criteria as well as specific criteria for operability in children with unrepaired systemic-to-pulmonary shunt lesions. Expand
Pediatric Pulmonary Hypertension.
TLDR
An overview of recent information regarding the current approach and diagnostic classification of PAH in children as based on discussions and recommendations from the Pediatric Task Force of the 5th World Symposium on Pulmonary Hypertension (WSPH) in Nice, France is provided. Expand
Diagnosis, Evaluation and Treatment of Pulmonary Arterial Hypertension in Children
TLDR
A description of select etiologies of PH seen in pediatrics and an update on the most recent data pertaining to evaluation and management of children with PH/PAH are provided. Expand
Persistent Challenges in Pediatric Pulmonary Hypertension.
TLDR
A brief review highlights several key topics reflecting recent advances in the field and identifies persistent gaps in the understanding of clinical pediatric pulmonary hypertension. Expand
Management of Pulmonary Arterial Hypertension in the Pediatric Patient
TLDR
Care should be provided at centers with specialized expertise in the diagnosis and treatment of pediatric PAH by providers who understand the appropriate diagnostic algorithms, classification schemes, and treatment approaches. Expand
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An overview of recent information regarding the current approach and diagnostic classification of PAH in children as based on discussions and recommendations from the Pediatric Task Force of the 5th World Symposium on Pulmonary Hypertension (WSPH) in Nice, France is provided. Expand
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A comprehensive review of the diagnostic work-up of the child with suspected PAH as well as a review of some of the challenges faced when assessing a child for PAH are provided. Expand
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The concepts of perinatal maladaptation, maldevelopment and pulmonary hypoplasia as causative factors in pediatric pulmonary hypertension are emphasized and the importance of genetic, chromosomal and multiple congenital malformation syndromes in the presentation of Pediatrics pulmonary hypertension is highlighted. Expand
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